Chinese expert consensus on surgical treatment of congenital tracheal stenosis in children

Title: Chinese expert consensus on surgical treatment of congenital tracheal stenosis in children
Edition: Original
Classification: Experts consensus
Field: Diagnosis and Treatment
Countries and regions: China
Guidelines users: 儿童心胸外科医生、呼吸科医生、急诊科医生、重症监护医生
Evidence classification method: Grade A data comes from multiple randomized clinical trials or meta-analyses. Grade B data comes from single randomized clinical trials or multiple non-randomized trials. Grade C data comes from expert consensus, Case Studies, and/or small trial results
Development unit: Shanghai Children's Medical Center Affiliated to Shanghai Jiao Tong University School of Medicine
Registration time: 2022-05-24
Registration number: IPGRP-2022CN290
Purpose of the guideline: 儿童先天性气管狭窄(congenital tracheal stenosis,CTS)是一种因气管自身发育存在病理问题而致的先天性梗阻性气道疾病,婴幼儿期即可发病,常表现为反复的肺部感染和呼吸困难,甚至呼吸衰竭,如不及时治疗,死亡率高达50-80%。外科手术是目前CTS最主要的治疗方式。2003年开始,CTS的外科诊治技术在我国逐步推广应用,但至今国内外尚无统一标准,诊疗水平和治疗效果参差不齐,故国内相关领域的专家迫切需要集思广益,达成共识,从而来规范国内CTS患儿的诊疗行为、完善诊疗体系。